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<article article-type="research-article" dtd-version="1.3" xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xml:lang="ru"><front><journal-meta><journal-id journal-id-type="publisher-id">clinicaloncology</journal-id><journal-title-group><journal-title xml:lang="ru">Клинический случай в онкологии</journal-title><trans-title-group xml:lang="en"><trans-title>Clinical Case in Oncology</trans-title></trans-title-group></journal-title-group><issn pub-type="ppub">3034-1477</issn><issn pub-type="epub">3034-4018</issn><publisher><publisher-name>ОНКОПРАКТИК</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="doi">10.62546/3034-1477-2025-3-3-39-47</article-id><article-id custom-type="elpub" pub-id-type="custom">clinicaloncology-135</article-id><article-categories><subj-group subj-group-type="heading"><subject>Research Article</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="ru"><subject>КЛИНИЧЕСКИЕ СЛУЧАИ</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="en"><subject>CASE REPORTS</subject></subj-group></article-categories><title-group><article-title>Клинический случай успешного лечения гигантской саркоматоидной карциномы кожи заушной области</article-title><trans-title-group xml:lang="en"><trans-title>Clinical case of a giant sarcomatoid carcinoma of the skin arising in the postauricular area</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0009-0007-6393-7561</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Герк</surname><given-names>И. А.</given-names></name><name name-style="western" xml:lang="en"><surname>Gerk</surname><given-names>Ivan A.</given-names></name></name-alternatives><bio xml:lang="ru"><p>198255, Санкт-Петербург, пр. Ветеранов, д. 56</p></bio><bio xml:lang="en"><p>56 Veteranov Ave., St. Petersburg, 198255</p></bio><email xlink:type="simple">dr.ivangerk@gmail.com</email><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0003-4447-9458</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Орлова</surname><given-names>Р. В.</given-names></name><name name-style="western" xml:lang="en"><surname>Orlova</surname><given-names>Rashida V.</given-names></name></name-alternatives><bio xml:lang="ru"><p>198255, Санкт-Петербург, пр. Ветеранов, д. 56</p><p>199034, Санкт-Петербург, Университетская наб., д. 7/9 </p></bio><bio xml:lang="en"><p>56 Veteranov Ave., St. Petersburg, 198255</p><p>7/9 Universitetskaya Emb., St. Petersburg, 199034</p></bio><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0009-0007-3344-9022</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Иткин</surname><given-names>И. М.</given-names></name><name name-style="western" xml:lang="en"><surname>Itkin</surname><given-names>Ilya M.</given-names></name></name-alternatives><bio xml:lang="ru"><p>198255, Санкт-Петербург, пр. Ветеранов, д. 56</p></bio><bio xml:lang="en"><p>56 Veteranov Ave., St. Petersburg, 198255</p></bio><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0002-4587-4153</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Погребняков</surname><given-names>В. Ю.</given-names></name><name name-style="western" xml:lang="en"><surname>Pogrebnyakov</surname><given-names>Vladimir Yu.</given-names></name></name-alternatives><bio xml:lang="ru"><p>198255, Санкт-Петербург, пр. Ветеранов, д. 56</p></bio><bio xml:lang="en"><p>56 Veteranov Ave., St. Petersburg, 198255</p></bio><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Хрусталев</surname><given-names>М. И.</given-names></name><name name-style="western" xml:lang="en"><surname>Khrustalev</surname><given-names>Mikhail I.</given-names></name></name-alternatives><bio xml:lang="ru"><p>198255, Санкт-Петербург, пр. Ветеранов, д. 56</p></bio><bio xml:lang="en"><p>56 Veteranov Ave., St. Petersburg, 198255</p></bio><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0002-1899-554X</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Ермакова</surname><given-names>Т. С.</given-names></name><name name-style="western" xml:lang="en"><surname>Ermakova</surname><given-names>Tatyana S.</given-names></name></name-alternatives><bio xml:lang="ru"><p>198255, Санкт-Петербург, пр. Ветеранов, д. 56</p></bio><bio xml:lang="en"><p>56 Veteranov Ave., St. Petersburg, 198255</p></bio><xref ref-type="aff" rid="aff-1"/></contrib></contrib-group><aff-alternatives id="aff-1"><aff xml:lang="ru"><institution>СПб ГБУЗ «Городской клинический онкологический диспансер»</institution><country>Россия</country></aff><aff xml:lang="en"><institution>City Clinical Oncological Dispensary</institution><country>Russian Federation</country></aff></aff-alternatives><aff-alternatives id="aff-2"><aff xml:lang="ru"><institution>СПб ГБУЗ «Городской клинический онкологический диспансер»; ФГБОУ ВО «Санкт-Петербургский государственный университет»</institution><country>Россия</country></aff><aff xml:lang="en"><institution>City Clinical Oncological Dispensary; St. Petersburg State University</institution><country>Russian Federation</country></aff></aff-alternatives><pub-date pub-type="collection"><year>2025</year></pub-date><pub-date pub-type="epub"><day>28</day><month>01</month><year>2026</year></pub-date><volume>3</volume><issue>3</issue><fpage>39</fpage><lpage>47</lpage><permissions><copyright-statement>Copyright &amp;#x00A9; Герк И.А., Орлова Р.В., Иткин И.М., Погребняков В.Ю., Хрусталев М.И., Ермакова Т.С., 2026</copyright-statement><copyright-year>2026</copyright-year><copyright-holder xml:lang="ru">Герк И.А., Орлова Р.В., Иткин И.М., Погребняков В.Ю., Хрусталев М.И., Ермакова Т.С.</copyright-holder><copyright-holder xml:lang="en">Gerk I.A., Orlova R.V., Itkin I.M., Pogrebnyakov V.Y., Khrustalev M.I., Ermakova T.S.</copyright-holder><license xml:lang="ru" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>Данная работа распространяется под лицензией Creative Commons Attribution 4.0.</license-p></license><license xml:lang="en" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>This work is licensed under a Creative Commons Attribution 4.0 License.</license-p></license></permissions><self-uri xlink:href="https://www.oncocase.ru/jour/article/view/135">https://www.oncocase.ru/jour/article/view/135</self-uri><abstract><p>Саркоматоидная карцинома кожи — редкий и агрессивный вариант плоскоклеточного рака кожи с низкой дифференцировкой. Из-за малочисленности наблюдений отсутствуют стандартизированные подходы к диагностике и лечению, что придает особую ценность описанию клинических случаев. В статье представлен опыт лечения молодого пациента с саркоматоидной карциномой кожи заушной области, которая характеризовалась быстрым ростом до гигантских размеров, распадом и кровотечением. В ходе комплексного лечения, включающего хирургию и химиоиммунотерапию, злокачественный процесс был взят под контроль, и в настоящий момент у пациента отсутствуют клинические и рентгенологические признаки опухоли.</p></abstract><trans-abstract xml:lang="en"><p>Sarcomatoid carcinoma of the skin is a rare and aggressive variant of cutaneous squamous cell carcinoma characterized by poor differentiation. Due to the limited number of reported cases, there are no standardized approaches to management, making individual case reports particularly valuable. We describe a young patient presenting with a rapidly enlarging giant sarcomatoid carcinoma of the postauricular region with ulceration and bleeding. A combinedmodality treatment, including surgery and chemoimmunotherapy, resulted in complete clinical and radiological disease control, with no evidence of recurrence at follow-up.</p></trans-abstract><kwd-group xml:lang="ru"><kwd>саркоматоидная карцинома кожи</kwd><kwd>плоскоклеточный рак кожи</kwd></kwd-group><kwd-group xml:lang="en"><kwd>sarcomatoid carcinoma of the skin</kwd><kwd>cutaneous squamous cell carcinoma</kwd></kwd-group></article-meta></front><back><ref-list><title>References</title><ref id="cit1"><label>1</label><citation-alternatives><mixed-citation xml:lang="ru">Shafi S., Gru A.A., Roman J. et al. A Case Series of Primary Cutaneous Sarcomatoid Carcinoma With Aberrant Smooth Muscle Actin Expression: A Clinicopathologic and Immunophenotypic Study // Am.J.Dermatopathol. 2025. Vol. 47, No. 2. Р. 83–92. 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